Thrombocytemia

Thrombocytemia

Thrombocythemia yog ib qho kev loj hlob ntawm cov ntshav platelets, nrog rau qhov tshwm sim ntawm kev pheej hmoo ntawm thrombosis (ntshav txhaws). Nws raug txheeb xyuas los ntawm cov qauv ntshav lossis cov pob txha pob txha. Nws yog kho nrog tshuaj aspirins los yog anti-platelets.

Thrombocythemia, yog dab tsi?

Lus txhais

Thrombocythemia yog ib pawg kab mob ntshav. Lawv feem ntau txhawj xeeb txog cov ntshav platelets, cov hlwb tsim los ntawm cov pob txha pob txha thiab nws lub luag haujlwm yog txhawm rau txhaws cov ntshav (ua kom nws muaj zog dua).

Thaum lub sij hawm ib tug thrombocythemia, zus tau tej cov qia hlwb nyob rau hauv cov pob txha pob txha yog txawv txav, nws ua rau lub proliferation ntawm cov ntshav platelet hlwb. Txawm li cas los xij, lawv lub luag haujlwm yog coagulation ntawm cov ntshav, qhov kev loj hlob no ua rau muaj kev pheej hmoo ntau ntxiv ntawm cov hlab ntsha: thrombosis.

Ntawm qhov tsawg dua, thrombocythemia tuaj yeem ua rau los ntshav yam tsis muaj kev raug mob tshwm sim.

Kev phom sij rau tus neeg mob

Nws yog tshwj xeeb yog qhov tshwm sim ntawm thrombocythemia uas yuav tsum tau ntshai. Thrombosis tseem yog ib qho tseem ceeb ntawm kev tuag. Qhov nruab nrab ciaj sia taus ntawm ib tug neeg uas tsis kho thrombocythemia yog 12 mus rau 15 xyoo, tab sis nws txawv heev nyob ntawm seb cov thrombosis.

Lwm qhov laj thawj loj yog qhov pom ntawm hemorrhages, (tshwj xeeb tshaj yog ntawm daim tawv nqaij lossis hauv cov mucous daim nyias nyias). Thrombocythemia tuaj yeem ua rau lub qhov ntswg, cov pos hniav, bruising los ntawm cov pob me me, lossis cov ntshav hauv cov zis.

Ua rau thrombocythemia

Muaj ob hom thrombocythemia:

  • Reactions, uas yog nyob rau hauv cov tshuaj tiv thaiv rau ib tug cloudiness. Cov kab mob no tuaj yeem ua rau ntau hom kab mob, xws li kab mob, o, kev ntxhov siab hnyav, tsis muaj hlau hauv cov ntshav, lossis qog nqaij hlav.
  • Qhov tseem ceeb, hauv 10 txog 20% ​​ntawm cov neeg mob, uas tshwm sim yam tsis muaj keeb kwm tsim. Lawv yog ib feem ntawm myeloproliferative syndromes.

Ntsuas nws

Kev kuaj mob ntawm thrombocythemia yog ua los ntawm cov ntshav kuaj. Qhov chaw pib raug soj ntsuam ntawm qib platelet ntau dua 450 ib microliter, nrog rau qhov tsis zoo. Qhov kev kuaj mob no tuaj yeem ua tau yooj yim los ntawm kev kuaj ntshav niaj hnub thaum pub ntshav lossis kuaj mob.

Kev kuaj caj ces tuaj yeem ua kom pom tus kab mob.

Qee lub sij hawm yuav tsum tau kuaj xyuas cov pob txha pob txha (cov qauv sau) los kuaj cov qia cell.

Risk yam tseem ceeb

Thrombocythemia feem ntau cuam tshuam rau cov neeg laus hnub nyoog ntawm 50 thiab 70 xyoo, nrog rau cov poj niam hluas. Cov neeg mob uas muaj hnub nyoog tshaj 60 xyoo tuaj yeem muaj kev pheej hmoo siab yog tias lawv muaj keeb kwm ntawm thrombosis (ntshav txhaws) lossis lwm yam mob ntshav. Txawm li cas los xij, kev suav platelet siab tsis yog qhov qhia txog kev pheej hmoo.

Paub cov tsos mob ntawm thrombocythemia

Tsis muaj cov tsos mob tshwm sim tiag tiag ntawm thrombocythemia, tab sis ob peb lub ntsiab lus sawv tawm:

  • Kev hnov ​​​​mob, liab, tingling ntawm lub cev ntawm lub cev (tes, taw), los yog qhov sib txawv ntawm cov ntiv tes txias.
  • Mob hauv siab
  • Qhov tshwm sim ntawm qhov pom ntawm qhov muag
  • Tsis muaj zog ntawm lub cev, kiv taub hau
  • mob taub hau
  • Los ntshav (nquag bruising, los ntshav qhov ntswg, rhiab pos hniav)

Txoj hauv kev zoo tshaj plaws yog saib xyuas koj cov ntshav platelet suav thaum lub sijhawm kuaj niaj hnub. Nws kwv yees tias ib nrab ntawm thrombocythemia raug kuaj pom yam tsis muaj tus neeg mob txawm yws txog cov tsos mob.

Kev kho mob ntawm thrombocythemia

tshuaj aspirin

Feem ntau ntawm cov mob thrombocythemia yog kho nrog tshuaj aspirin, rau nws cov khoom tiv thaiv coagulant, txo qhov kev pheej hmoo ntawm thrombosis, nrog rau txo cov tsos mob.

Anti-platelets

Cov tshuaj xws li hydroxyurea thiab anagrelides los yog interferon-alpha tau noj kom txog thaum cov ntshav platelet suav rov qab zoo li qub.

Thrombacytaphérèse

Thaum muaj xwm txheej ceev, piv txwv li yog tias platelet suav ntau dhau, thrombacytapheresis tuaj yeem ua tau. Lub hom phiaj ntawm kev ua haujlwm yog kom tshem tawm cov neeg mob cov ntshav, tshem tawm cov ntshav platelets ua ntej rov txhaj tshuaj yam tsis muaj nws cov platelets.

Cov mob hnyav tshaj plaws kuj tseem tuaj yeem nrog kev hloov pauv ntawm cov qia rau ib tug hluas.

Raws li tus kab mob no kho tsis tau ntau zaus, koj yuav tsum tau siv cov tshuaj tiv thaiv coagulant no tsis tu ncua rau tag nrho koj lub neej.

Tiv thaiv thrombocythemia

Tsis zoo li reactive thrombocythemia, uas tshwm sim tom qab lwm yam kab mob, qhov tseem ceeb muaj keeb kwm uas tseem nyuaj rau kev nkag siab, thiab yog li tsis muaj kev tiv thaiv zoo tiag tiag.

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